rospedРоссийский педиатрический журнал имени М.Я. СтуденикинаM.Ya. Studenikin Russian Pediatric JournalФГАУ «НМИЦ здоровья детей» Минздрава России10.46563/1560-9561-2023-26-2-145-148qqnwdzrosped-26Research ArticleКЛИНИЧЕСКИЙ СЛУЧАЙCLINICAL CASEРедкий случай сочетания тотального аномального дренажа лёгочных вен с врождённой лимфангиэктазией лёгкихA rare case of the combination of total abnormal pulmonary vein drainage with congenital lung lymphangiectasiahttps://orcid.org/0000-0002-7512-3991СарсенбаеваГульжан ИскендировнаSarsenbayevaGulzhan I.

Канд. мед. наук, кардиохирург, АО «Научный центр педиатрии и детской хирургии» Минздрава Республики Казахстан

e-mail: gulzhan75@mail.ru 

MD, PhD, cardiac surgeon, Scientific Center of Pediatrics and Pediatric Surgery, Almaty, 050044, Republic of Kazakhstan.

e-mail: gulzhan75@mail.ru

gulzhan75@mail.ruhttps://orcid.org/0000-0002-7780-6243СадыковаАлтынай ЖенисовнаSadykovaAltynay Zh.

Магистр медицины, неонатолог отделения неонатологии и хирургии новорожденных, АО «Научный центр педиатрии и детской хирургии» Минздрава Республики Казахстан

noemail@neicon.ruБердибековАлмас БекболатовичBerdibekovAlmas B.

Зав. отделением кардио­хирургии и интервенционной кардиологии, АО «Научный центр педиатрии и детской хирургии» Минздрава Республики Казахстан

noemail@neicon.ruХасановаОлеся ЗакировнаKhasanovaOlesya Z.

Врач патологоанатом, Городское патологоанатомическое бюро УОЗ г. Алматы, Казахстан

noemail@neicon.ruАО «Научный центр педиатрии и детской хирургии» Минздрава Республики КазахстанScientific Center of Pediatrics and Pediatric SurgeryГородское патологоанатомическое бюро УОЗ г. АлматыMunicipal Pathoanatomical Bureau202309082023232145148Copyright © Сарсенбаева Г.И., Садыкова А.Ж., Бердибеков А.Б., Хасанова О.З., 20232023Сарсенбаева Г.И., Садыкова А.Ж., Бердибеков А.Б., Хасанова О.З.Sarsenbayeva G.I., Sadykova A.Z., Berdibekov A.B., Khasanova O.Z.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.rosped.ru/jour/article/view/26

В статье описан клинический случай сочетания у новорождённого врождённого порока сердца — тотального аномального дренажа лёгочных вен в правое предсердие с врождённым пороком лёгких — лимфангиэктазией. Выявлено влияние экстракардиальной патологии на течение и исход кардиохирургической операции и сложность ранней диагностики редкой патологии лёгких.

Участие авторов

Участие авторов:Сарсенбаева Г.И. — концепция и дизайн исследования, написание и редактирование текста;Садыкова А.Ж., Бердибеков А.Б., Хасанова О.З. — сбор и обработка материала.Все соавторы — утверждение окончательного варианта статьи, ответственность за целостность всех частей статьи.

Финансирование

Финансирование. Исследование не имело финансовой поддержки.

Конфликт интересов

Конфликт интересов. Авторы заявляют об отсутствии конфликта интересов. 

Поступила 16

Поступила 16.02.2023Принята к печати 21.03.2023Опубликована 28.04.2023

The article describes a clinical report of a combination of congenital heart disease due to total anomalous pulmonary venous drainage into the right atrium with congenital lung disease — lymphoangiectasia in a newborn infant. The role of extracardiac pathology on the course and outcome of cardiac surgery and the complexity of early diagnosis of a rare lung pathology are presented.

Contributors

Contributors:Sarsenbayeva G.I. — concept and design of the study;Sadykova A.Zh., Berdibekov A.B., Khasanova O.Z. — collection and processing of the material;Sarsenbayeva G.I. — writing and editing of the text.All co-authors — approval of the final version of the article, responsibility for the integrity of all parts of the article.

Acknowledgment

Acknowledgment. The study had no sponsorship.

Conflict of interest

Conflict of interest. The authors declare no conflict of interest.

Received

Received:  February 16, 2023Accepted: March 21, 2023Published: April 28, 2023

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The authors declare that there are no conflicts of interest present.