rospedРоссийский педиатрический журнал имени М.Я. СтуденикинаM.Ya. Studenikin Russian Pediatric JournalФГАУ «НМИЦ здоровья детей» Минздрава России10.46563/1560-9561-2023-26-4-242-251ivbhwhrosped-43Research ArticleОРИГИНАЛЬНЫЕ ИССЛЕДОВАНИЯORIGINAL INVESTIGATIONSДиагностика и лечение лимфатических мальформаций: опыт хирургического отделения новорождённых и детей грудного возрастаDiagnosis and treatment of lymphatic malformations: experience of the surgical department for newborns and infantshttps://orcid.org/0000-0001-8663-2698ГурскаяАлександра СергеевнаGurskayaAleksandra S.

Канд. мед. наук, зав. хирургическим отд-нием новорождённых и детей грудного возраста ФГБУ «НМИЦ здоровья детей» Минздрава России.

e-mail: gurskaya.as@nczd.ru

noemail@neicon.ruhttps://orcid.org/0000-0001-9889-6295СулавкоМария АлександровнаSulavkoMariya A.

Врач — детский хирург хирургического отд-ния новорож­дённых и детей грудного возраста.

e-mail: sulavko.ma@nczd.ru

Pediatric surgeon, Department of neonatal and pediatric surgery, National Medical Research Center for Children’s Health, Moscow, 119991, Russian Federation.

e-mail: sulavko.ma@nczd.ru

sulavko.ma@nczd.ruhttps://orcid.org/0000-0002-2809-1894БаязитовРимир РадиковичBayazitovRimir R.

Канд. мед. наук, врач – детский хирург хирургического отд-ния новорождённых и детей грудного возраста ФГБУ «НМИЦ здоровья детей» Минздрава Росси.

e-mail: bayazitov.rr@nczd.ru

noemail@neicon.ruhttps://orcid.org/0000-0001-5098-2266ЕкимовскаяЕкатерина ВикторовнаEkimovskayaEkaterina V.

Канд. мед. наук, врач — детский хирург хирургического отделения новорождённых и детей грудного возраста ФГБУ «НМИЦ здоровья детей» Минздрава России.

e-mail: ekimovskaia.ev@nczd.ru

noemail@neicon.ruhttps://orcid.org/0000-0002-5320-837XНаковкинОлег НиколаевичNakovkinOleg N.

Зав. отделением реанимации и интенсивной терапии новорождённых и детей грудного возраста ФГБУ «НМИЦ здоровья детей» Минздрава России.

e-mail: nakovkin.on@nczd.ru

noemail@neicon.ruhttps://orcid.org/0000-0002-1707-102XКарнутаИнна ВикторовнаKarnutaInna V.

Врач — детский хирург хирургического отделения новорождённых и детей грудного возраста ФГБУ «НМИЦ здоровья детей» Минздрава России.

e-mail: karnuta.iv@nczd.ru

noemail@neicon.ruhttps://orcid.org/0000-0002-3717-9281КлепиковаАнна АлексеевнаKlepikovaAnna A.

Врач-неонатолог хирургического отделения новорожденных и детей грудного возраста ФГБУ «НМИЦ здоровья детей» Минздрава России.

e-mail: klepikova.aa@nczd.ru

noemail@neicon.ruhttps://orcid.org/0000-0002-7846-3473СагоянГарик БорисовичSagoyanGarik B.

Врач — детский онколог детского онкологического отделения № 1 ФГБУ «НМЦ онкологии им. Н.Н. Блохина» Минздрава России.

e-mail: sagoyan-garik@mail.ru

noemail@neicon.ruhttps://orcid.org/0000-0001-7944-8438ХагуровРуслан АслановичHagurovRuslan A.

Канд. мед. наук, врач — детский хирург отд-ния микрохирургии ГБУЗ «ДГКБ им. Н.Ф. Филатова» Департамента здравоохранения города Москвы.

e-mail: hagurov@gmail.com

noemail@neicon.ruhttps://orcid.org/0000-0001-8586-7946ФисенкоАндрей ПетровичFisenkoAndrey P.

Доктор мед. наук, проф., директор ФГБУ «НМИЦ здоровья детей» Минздрава России.

e-mail: director@nczd.ru

noemail@neicon.ruФГБУ «Национальный медицинский исследовательский центр здоровья детей» Минздрава РоссииРоссияNational Medical Research Center for Children’s HealthRussian FederationФГБУ «Национальный медицинский центр онкологии им. Н.Н. Блохина» Минздрава РоссииРоссияN.N. Blokhin National Medical Research Center of OncologyRussian FederationГБУЗ «Детская городская клиническая больница им. Н.Ф. Филатова» Департамента здравоохранения города МосквыРоссияN.F. Filatov Children’s City HospitalRussian Federation202313092023264242251Copyright © Гурская А.С., Сулавко М.А., Баязитов Р.Р., Екимовская Е.В., Наковкин О.Н., Карнута И.В., Клепикова А.А., Сагоян Г.Б., Хагуров Р.А., Фисенко А.П., 20232023Гурская А.С., Сулавко М.А., Баязитов Р.Р., Екимовская Е.В., Наковкин О.Н., Карнута И.В., Клепикова А.А., Сагоян Г.Б., Хагуров Р.А., Фисенко А.П.Gurskaya A.S., Sulavko M.A., Bayazitov R.R., Ekimovskaya E.V., Nakovkin O.N., Karnuta I.V., Klepikova A.A., Sagoyan G.B., Hagurov R.A., Fisenko A.P.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.rosped.ru/jour/article/view/43Введение

Введение. Лимфатические мальформации (ЛМФ) являются врождённой патологией лимфатических сосудов, возникшей в процессе эмбриогенеза. Актуальность темы обусловлена редкостью этих форм патологии, разнообразием клинических проявлений, отсутствием клинических рекомендаций по лечению.

Цель

Цель: анализ собственного опыта диагностики и лечения ЛМФ в хирургическом отделении новорождённых и детей грудного возраста.

Материалы и методы

Материалы и методы. Проведён ретроспективный анализ 27 историй болезни детей с различными формами ЛМФ за 2017–2022 гг.

Результаты

Результаты. В зависимости от формы ЛМФ детям проводились консервативная терапия, склерозирование или радикальное удаление образования.

Выводы

Выводы. Проведение генетического анализа на спектр синдромов избыточного роста необходимо всем пациентам с ЛМФ для уточнения этиологии процесса, предотвращения рецидивирования и профилактики осложнений.

Участие авторов

Участие авторов:Гурская А.С. — концепция и дизайн исследования;Сулавко М.А., Наковкин О.Н., Карнута И.В., Баязитов Р.Р., Екимовская Е.В, Хагуров Р.А., Сагоян Г.Б. — сбор и обработка материала;Гурская А.С., Сулавко М.А., Екимовская Е.В., Фисенко А.П. — написание текста, редактирование.Все соавторы — утверждение окончательного варианта статьи, ответственность за целостность всех частей статьи.

Финансирование

Финансирование. Исследование не имело финансовой поддержки.

Конфликт интересов

Конфликт интересов. Авторы заявляют об отсутствии конфликта интересов.

Поступила 19

Поступила 19.05.2023Принята к печати 20.06.2023Опубликована 31.08.2023

Introduction

Introduction. Lymphatic malformations (LM) are a congenital pathology of lymphatic vessels that arose during embryogenesis. The relevance of the research topic is due to the rarity, variety of clinical manifestations, and the lack of clinical recommendations for treatment. Aim. To evaluate our experience of surgical and conservative treatment of LM in the surgical department for newborns and infants.

Materials and methods

Materials and methods. We performed a retrospective analysis of infants with various forms of LM treated at our department from 2017 to 2022. The study protocol was approved by the local ethics committee. The patients’ parents gave written voluntary informed consent to participate in the study.

Results

Results. Depending on the form of a LM, the infants underwent conservative therapy, sclerotherapy or surgical resection of the LM.

Conclusions

Conclusions. Genetic tests for the spectrum of overgrowth syndromes are necessary for all LM patients to clarify the etiology of the process, prevent recurrence and complications.

Contribution

Contribution:Gurskaya A.S. — concept and design of the study;Sulavko M.A., Nakovkin O.N., Karnuta I.V., Bayazitov R.R., Ekimovskaya E.V., Khagurov R.A., Sagoyan G.B. — collection and processing of material;Gurskaya A.S., Sulavko M.A., Ekimovskaya E.V., Fisenko A.P. — writing and editing the text.All co-authors — approval of the final version of the article, responsibility for the integrity of all parts of the article.

Acknowledgment

Acknowledgment. The study had no sponsorship.

Conflict of interest

Conflict of interest. The authors declare no conflict of interest.

Received

Received: May 19, 2023Accepted: June 20, 2023Published: August 31, 2023

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The authors declare that there are no conflicts of interest present.