Diagnosis and treatment of lymphatic malformations: experience of the surgical department for newborns and infants
https://doi.org/10.46563/1560-9561-2023-26-4-242-251
EDN: ivbhwh
Abstract
Introduction. Lymphatic malformations (LM) are a congenital pathology of lymphatic vessels that arose during embryogenesis. The relevance of the research topic is due to the rarity, variety of clinical manifestations, and the lack of clinical recommendations for treatment. Aim. To evaluate our experience of surgical and conservative treatment of LM in the surgical department for newborns and infants.
Materials and methods. We performed a retrospective analysis of infants with various forms of LM treated at our department from 2017 to 2022. The study protocol was approved by the local ethics committee. The patients’ parents gave written voluntary informed consent to participate in the study.
Results. Depending on the form of a LM, the infants underwent conservative therapy, sclerotherapy or surgical resection of the LM.
Conclusions. Genetic tests for the spectrum of overgrowth syndromes are necessary for all LM patients to clarify the etiology of the process, prevent recurrence and complications.
Contribution:
Gurskaya A.S. — concept and design of the study;
Sulavko M.A., Nakovkin O.N., Karnuta I.V., Bayazitov R.R., Ekimovskaya E.V., Khagurov R.A., Sagoyan G.B. — collection and processing of material;
Gurskaya A.S., Sulavko M.A., Ekimovskaya E.V., Fisenko A.P. — writing and editing the text.
All co-authors — approval of the final version of the article, responsibility for the integrity of all parts of the article.
Acknowledgment. The study had no sponsorship.
Conflict of interest. The authors declare no conflict of interest.
Received: May 19, 2023
Accepted: June 20, 2023
Published: August 31, 2023
About the Authors
Aleksandra S. GurskayaRussian Federation
Mariya A. Sulavko
Russian Federation
Pediatric surgeon, Department of neonatal and pediatric surgery, National Medical Research Center for Children’s Health, Moscow, 119991, Russian Federation.
e-mail: sulavko.ma@nczd.ru
Rimir R. Bayazitov
Russian Federation
Ekaterina V. Ekimovskaya
Russian Federation
Oleg N. Nakovkin
Russian Federation
Inna V. Karnuta
Russian Federation
Anna A. Klepikova
Russian Federation
Garik B. Sagoyan
Russian Federation
Ruslan A. Hagurov
Russian Federation
Andrey P. Fisenko
Russian Federation
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Review
For citations:
Gurskaya A.S., Sulavko M.A., Bayazitov R.R., Ekimovskaya E.V., Nakovkin O.N., Karnuta I.V., Klepikova A.A., Sagoyan G.B., Hagurov R.A., Fisenko A.P. Diagnosis and treatment of lymphatic malformations: experience of the surgical department for newborns and infants. Russian Pediatric Journal. 2023;26(4):242-251. (In Russ.) https://doi.org/10.46563/1560-9561-2023-26-4-242-251. EDN: ivbhwh