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Primary immunodeficiency in the 9-year child

https://doi.org/10.46563/1560-9561-2023-26-6-455-458

EDN: oqipgt

Abstract

Primary immunodeficiency conditions are a heterogeneous group of disorders caused by defects in various parts of the immune system, manifested in the form of recurrent infectious and autoimmune diseases of varying severity. The authors describe own clinical observation to determine the principles of diagnosis and treatment of primary immunodeficiency in children in modern conditions. The average age of diagnosis of an immunodeficiency condition has been established to be best over 30 days, but often this time increases to several years. The data of the enrolment of primary immunodeficiency states of the Republic of Dagestan on the diagnosis and permanent replacement therapy of immunodeficiency states is also presented.

Acknowledgment. The study had no sponsorship.

Conflict of interest. The authors declare no conflict of interest.

Contribution:
Aliskandieva Z.A. — concept and design of the study, statistical processing of the material;
Idrisova R.M., Amirova K.M. — collection and processing of material;
Aliskandieva Z.A. — writing the text;
Aliskandiev A.M., Israilov M.I. — editing the text.
All co-authors — approval of the final version of the article, responsibility for the integrity of all parts of the article.

Received: October 16, 2023
Accepted: November 28, 2023
Published: December 27, 2023

About the Authors

Zuleykha A. Aliskandieva
Dagestan State Medical University
Russian Federation

MD, PhD, Associate Prof. of the Department of Faculty and Hospital Pediatrics, Pediatrics of the FPC and Teaching Staff of the Dagestan State Medical University, Dagestan State Medical University, Makhachkala, 367000, Russian Federation

e-mail: aliskandieva@mail.ru



Alaudin M. Aliskandiev
Dagestan State Medical University
Russian Federation


Rakhmat M. Idrisova
Dagestan State Medical University
Russian Federation


Magomed I. Izrailov
Dagestan State Medical University
Russian Federation


Kistaman М. Amirova
Dagestan State Medical University
Russian Federation


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Review

For citations:


Aliskandieva Z.A., Aliskandiev A.M., Idrisova R.M., Izrailov M.I., Amirova K.М. Primary immunodeficiency in the 9-year child. Russian Pediatric Journal. 2023;26(6):455-458. (In Russ.) https://doi.org/10.46563/1560-9561-2023-26-6-455-458. EDN: oqipgt

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ISSN 1560-9561 (Print)
ISSN 2413-2918 (Online)